Axial propriospinal myoclonus misdiagnosed as myoclonic seizures

Propriospinal myoclonus is characterized by brief, repetitive, mainly arrhythmic myoclonic jerks arising from axial muscles and spreading rostrally and caudally to the adjacent myotomes. Propa gation is not an obligatory feature and jerks can remain localized to the axial muscles. We present a patient with an axial non-propagated propriospinal myoclonus, misdiagnosed as myoclo nic seizures, occurring at rest and at wake-sleep transition phase, and evoked by auditory and sensory stimuli. Video-polygraphic recording was useful for a correct differential diagnosis between epileptic and nonepileptic myoclonic events.