Scoring system for renal pathology in Fabry disease: report of the International Study Group of Fabry Nephropathy (ISGFN) | Zendy

Agnes B. Fogo | Zendy; Leif Bostad | Zendy; Einar Svarstad | Zendy; W. James Cook | Zendy; Solange Moll | Zendy; Frédéric Barbey | Zendy; Laurette Geldenhuys | Zendy; Michael L. West | Zendy; D Ferluga | Zendy; Bojan Vujkovac | Zendy; Alexander J. Howie | Zendy; A. Burns | Zendy; Roy Reeve | Zendy; Stephen Waldek | Zendy; LaureHélène Noël | Zendy; JeanPierre Grünfeld | Zendy; Carmen Valbuena | Zendy; João Paulo Oliveira | Zendy; J. Müller | Zendy; Frank Breunig | Zendy; X. Zhang | Zendy; David G. Warnock | Zendy

Open Access

Scoring system for renal pathology in Fabry disease: report of the International Study Group of Fabry Nephropathy (ISGFN)

Author(s) -

Agnes B. Fogo,

Leif Bostad,

Einar Svarstad,

W. James Cook,

Solange Moll,

Frédéric Barbey,

Laurette Geldenhuys,

Michael L. West,

D Ferluga,

Bojan Vujkovac,

Alexander J. Howie,

A. Burns,

Roy Reeve,

Stephen Waldek,

LaureHélène Noël,

JeanPierre Grünfeld,

Carmen Valbuena,

João Paulo Oliveira,

J. Müller,

Frank Breunig,

X. Zhang,

David G. Warnock

Publication year - 2009

Publication title -

nephrology dialysis transplantation

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 1.654

H-Index - 168

eISSN - 1460-2385

pISSN - 0931-0509

DOI - 10.1093/ndt/gfp528

Subject(s) - fabry disease , proteinuria , fabry's disease , medicine , renal function , nephropathy , renal pathology , kidney , pathology , urology , disease , endocrinology , diabetes mellitus

In Fabry nephropathy, alpha-galactosidase deficiency leads to accumulation of glycosphingolipids in all kidney cell types, proteinuria and progressive loss of kidney function.

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