Open AccessSudden cardiac death in Andersen–Tawil syndrome
Author(s) -
Stefan Peters,
Eric SchulzeBahr,
Susan P. Etheridge,
Martin TristaniFirouzi
Publication year - 2007
Publication title -
ep europace
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.119
H-Index - 102
eISSN - 1532-2092
pISSN - 1099-5129
DOI - 10.1093/europace/eul188
Subject(s) - medicine , periodic paralysis , cardiology , sudden cardiac death , ventricular tachycardia , paralysis , surgery
Andersen-Tawil syndrome (ATS) is an autosomal dominant or sporadic disorder characterized by periodic paralysis, dysmorphic features, and ventricular arrhythmias. Although ventricular tachycardia burden is quite high sudden cardiac death in ATS is rare. We describe a case with sudden cardiac death due to electrical storm a few days after ICD implantation in KCNJ2 mutation-negative ATS.
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