Sustained monomorphic ventricular tachycardia associated with unrepaired double-chambered right ventricle

Double-chambered right ventricle (DCRV) is a congenital anomaly characterized by the division of the ventricular cavity into two chambers separated by an abnormal hypertrophied muscular band or by severe hypertrophy of the muscle wall. Two adult patients with a diagnosis of DCRV presented sustained monomorphic ventricular tachycardia. In both cases, the clinical tachycardia was induced with programmed stimulation. After surgically resecting, the muscular band tachycardia could no longer be induced in the patient who underwent follow-up electrophysiological study. The outcome was favourable; there was no clinical recurrence of ventricular tachycardia in the two patients at 48 and 36 months, respectively.