Chronic Granulomatous Disease in Patients Reaching Adulthood: A Nationwide Study in France
Author(s) -
Bertrand Dunogué,
B. Pilmis,
Nizar Mahlaoui,
Caroline Elie,
Hélène Coignard-Biehler,
Karima Amazzough,
Nicolas Noël,
Hélène Salvator,
Émilie Catherinot,
LouisJean Couderc,
Harry Sokol,
Fanny Lanternier,
Fanny Fouyssac,
Julie Bardet,
Jacinta Bustamante,
MarieAnne GougerotPocidalo,
Vincent Barlogis,
A. Masseau,
I. Durieu,
Marc Lecuit,
Felipe Suárez,
Alain Fischer,
Stéphane Blanche,
Olivier Hermine,
Olivier Lortholary
Publication year - 2017
Publication title -
clinical infectious diseases
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 3.44
H-Index - 336
eISSN - 1537-6591
pISSN - 1058-4838
DOI - 10.1093/cid/ciw837
Subject(s) - medicine , chronic granulomatous disease , pediatrics , primary immunodeficiency , hematopoietic stem cell transplantation , retrospective cohort study , disease , young adult , transplantation , surgery , immunology
Although prognosis of Chronic Granulomatous Disease (CGD) has greatly improved, few studies have focused on its long-term outcome. We studied the clinical course and sequelae of CGD patients diagnosed before age 16, at various adult time points.
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