Bone marrow transplantation as treatment for X-linked immunodeficiency with hyper-IgM | Zendy

Pierre Bordigoni | Zendy; B Auburtin | Zendy; A-S Carret | Zendy; Anne Schuhmacher | Zendy; Humbert Jc | Zendy; Françoise Le Deist | Zendy; D Sommelet | Zendy

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Bone marrow transplantation as treatment for X-linked immunodeficiency with hyper-IgM

Author(s) -

Pierre Bordigoni,

B Auburtin,

A-S Carret,

Anne Schuhmacher,

Humbert Jc,

Françoise Le Deist,

D Sommelet

Publication year - 1998

Publication title -

bone marrow transplantation

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 1.609

H-Index - 127

eISSN - 1476-5365

pISSN - 0268-3369

DOI - 10.1038/sj.bmt.1701497

Subject(s) - medicine , busulfan , cyclophosphamide , bone marrow transplantation , severe combined immunodeficiency , transplantation , immunodeficiency , bone marrow , surgery , immunopathology , immunology , chemotherapy , immune system , biochemistry , chemistry , gene

We report a 10-year-old boy with a severe form of immunodeficiency with hyper-IgM who underwent successful bone marrow transplantation with his HLA-matched sister as donor. Busulfan (20 mg/kg) and cyclophosphamide (200 mg/kg) were used as conditioning. The post-transplant course was uneventful. He is alive 25 months later with full hematological and immunological reconstitution.

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