Open AccessChordoma in children: Case-report and review of literature
Author(s) -
JeanLouis Habrand,
Jean Datchary,
Stéphanie Bolle,
A. Beaudré,
Ludovic De Marzi,
Kévin Beccaria,
Dinu Stefan,
Jacques Grill,
R. Dendale
Publication year - 2016
Publication title -
reports of practical oncology and radiotherapy
Language(s) - English
Resource type - Journals
eISSN - 2083-4640
pISSN - 1507-1367
DOI - 10.1016/j.rpor.2015.10.007
Subject(s) - chordoma , medicine , etiology , radiation therapy , proton therapy , surgery , cervical spine , pediatrics , psychiatry
We report an exceptional case of a very late local failure in a 9-year-old boy presenting with a chordoma of the cranio-cervical junction. The child was initially treated with a combination of surgical resection followed by high dose photon-proton radiation therapy. This aggressive therapy allowed a 9-year remission with minimal side-effects. Unfortunately, he subsequently presented with a local failure managed with a second full-dose course of protons. The child died one year later from local bleeding of unclear etiology.