Terapêutica de ressincronização na miocardiopatia induzida pelo pacing ventricular direito em doente pediátrico
Author(s) -
Pedro Carmo,
Graça Nogueira,
Rui Anjos,
Pedro Adragão,
Diogo Cavaco,
Regina Ribeiras,
José Pedro Neves,
Maymone Martins
Publication year - 2011
Publication title -
revista portuguesa de cardiologia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.266
H-Index - 26
eISSN - 2174-2030
pISSN - 0870-2551
DOI - 10.1016/j.repc.2011.09.017
Subject(s) - medicine , cardiology , mitral regurgitation , heart failure , atrioventricular block , cardiac resynchronization therapy , dilated cardiomyopathy , ejection fraction , regurgitation (circulation) , cardiomyopathy , diastole , blood pressure
A 2-day-old male infant required a conventional VVI pacemaker for congenital atrioventricular block. Three years later, he developed progressive heart failure due to left ventricular (LV) dysfunction and mitral regurgitation despite optimized medical treatment, and a cardiac resynchronization therapy (CRT) device was implanted. This is the first Portuguese report of CRT in a pediatric patient. One-year echocardiographic follow-up showed that LV shortening fraction had improved and LV end-diastolic dimension and mitral regurgitation had decreased. New York Heart Association class had improved from III-IV to I at 1-year follow-up.
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