Gadolinium enhanced cardiovascular magnetic resonance in Anderson-Fabry disease Evidence for a disease specific abnormality of the myocardial interstitium | Zendy

James Moon | Zendy; Bhavesh Sachdev | Zendy; Andrew G. Elkington | Zendy; William J. McKenna | Zendy; Atul Mehta | Zendy; Dudley J. Pennell | Zendy; Philip J Leed | Zendy; Perry Elliott | Zendy

Open Access

Gadolinium enhanced cardiovascular magnetic resonance in Anderson-Fabry disease Evidence for a disease specific abnormality of the myocardial interstitium

Author(s) -

James Moon,

Bhavesh Sachdev,

Andrew G. Elkington,

William J. McKenna,

Atul Mehta,

Dudley J. Pennell,

Philip J Leed,

Perry Elliott

Publication year - 2003

Publication title -

european heart journal

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 4.336

H-Index - 293

eISSN - 1522-9645

pISSN - 0195-668X

DOI - 10.1016/j.ehj.2003.09.017

Subject(s) - medicine , cardiology , myocardial infarction , magnetic resonance imaging , left ventricular hypertrophy , myocardial fibrosis , ejection fraction , muscle hypertrophy , hypertrophic cardiomyopathy , fibrosis , abnormality , hypertensive heart disease , fabry disease , disease , heart failure , radiology , blood pressure , psychiatry

Anderson-Fabry Disease (AFD), an X-linked disorder of sphingolipid metabolism, is a cause of idiopathic left ventricular hypertrophy but the mechanism of hypertrophy is poorly understood. Gadolinium enhanced cardiovascular magnetic resonance can detect focal myocardial fibrosis. We hypothesised that hyperenhancement would be present in AFD.

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