Systemic Type I IFN Inflammation in Human ISG15 Deficiency Leads to Necrotizing Skin Lesions
Author(s) -
Marta Martín-Fernández,
María Bravo GarcíaMorato,
Conor Gruber,
Sara Murias Loza,
Muhammad Nasir Hayat Malik,
Fahad Alsohime,
Abdullah Alakeel,
Rita Valdéz,
Sofija Buta,
Guadalupe Buda,
Marcelo A. Martí,
Margarita Larralde,
Bertrand Boisson,
M. F. Prieto Rodríguez,
Xueer Qiu,
Maya Chrabieh,
Mohammed Al Ayed,
Saleh Al Muhsen,
Jigar V. Desai,
Elise M. N. Ferré,
Sergio D. Rosenzweig,
Blanca Amador-Borrero,
Luz Yadira BravoGallego,
Ruth Olmer,
Sylvia Merkert,
Montserrat Bret Zurita,
Amika K. Sood,
Abdulkarim Alrabiaah,
MohamadHani Temsah,
Rabih Halwani,
Michelle Hernández,
Frank Peßler,
JeanLaurent Casanova,
Jacinta Bustamante,
Michail S. Lionakis,
Dusan Bogunovic
Publication year - 2020
Publication title -
cell reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 6.264
H-Index - 154
eISSN - 2639-1856
pISSN - 2211-1247
DOI - 10.1016/j.celrep.2020.107633
Subject(s) - isg15 , inflammation , immunology , medicine , dermis , phenotype , interferon , interferon gamma , inflammasome , pathology , biology , cytokine , gene , genetics , ubiquitin
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