Marfan Syndrome: new diagnostic criteria, same anesthesia care? Case report and review
Author(s) -
Maria Rita Elmor de Araújo,
Céline Marques,
S. Freitas,
Rita SantaBárbara,
Joana Alves,
Célia Xavier
Publication year - 2014
Publication title -
brazilian journal of anesthesiology (english edition)
Language(s) - English
Resource type - Journals
eISSN - 2352-2291
pISSN - 0104-0014
DOI - 10.1016/j.bjane.2014.09.004
Subject(s) - medicine , pectus carinatum , surgery , aortic dissection , pneumothorax , anesthesia , aorta , pectus excavatum
Marfan's Syndrome (MFS) is a disorder of connective tissue, mainly involving the cardiovascular, musculoskeletal, and ocular systems. The most severe problems include aortic root dilatation and dissection. Anesthetic management is vital for the improvement on perioperative morbidity.
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