z-logo
open-access-imgOpen Access
Complete form of pachydermoperiostosis
Author(s) -
Mônica Larissa Padilha Honório,
Guilherme Holanda Bezerra,
Vivianne Lira da Câmara Costa
Publication year - 2019
Publication title -
anais brasileiros de dermatologia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.461
H-Index - 44
eISSN - 1806-4841
pISSN - 0365-0596
DOI - 10.1016/j.abd.2019.04.009
Subject(s) - medicine , hyperhidrosis , spinal osteoarthropathy , dermatology , hypertrophic osteoarthropathy , radiological weapon , acne , pathogenesis , disease , rare disease , pathology , surgery
Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is reported in a male patient with disease onset in adolescence, with compatible clinical and radiological findings, presenting the three cardinal findings as well as other associated manifestations, such as hyperhidrosis and acne.

The content you want is available to Zendy users.

Already have an account? Click here to sign in.
Having issues? You can contact us here
Accelerating Research

Address

John Eccles House
Robert Robinson Avenue,
Oxford Science Park, Oxford
OX4 4GP, United Kingdom