Open AccessDevelopment and Validation of a New Scoring System to Predict Survival in Patients With Myotonic Dystrophy Type 1
Author(s) -
Karim Wahbi,
Raphaël Porcher,
Pascal Laforêt,
Abdallah Fayssoil,
Henri Marc Bécane,
Arnaud Lazarus,
Maximilien Sochala,
Tanya Stojkovic,
Anthony Béhin,
Sarah Léonard-Louis,
Pauline Arnaud,
Denis Furling,
Vincent Probst,
Dominique Babuty,
Sybille Pellieux,
Nicolas Clémenty,
Guillaume Bassez,
Yann Péréon,
B. Eymard,
Denis Duboc
Publication year - 2018
Publication title -
jama neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 5.298
H-Index - 231
eISSN - 2168-6157
pISSN - 2168-6149
DOI - 10.1001/jamaneurol.2017.4778
Subject(s) - medicine , myotonic dystrophy , interquartile range , cohort , hazard ratio , neuromuscular disease , confidence interval , proportional hazards model , cardiology , disease
Life expectancy is greatly shortened in patients presenting with myotonic dystrophy type 1 (DM1), the most common neuromuscular disease. A reliable prediction of survival in patients with DM1 is critically important to plan personalized health supervision.
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