Open AccessAortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
Author(s) -
Hong Ju Shin,
Jae Seung Shin
Publication year - 2020
Publication title -
the korean journal of thoracic and cardiovascular surgery/daehan hyungbu oe'gwa haghoeji. hyungbu simjang hyeolgwan
Language(s) - English
Resource type - Journals
eISSN - 2093-6516
pISSN - 0301-2859
DOI - 10.5090/kjtcs.2020.53.3.144
Subject(s) - medicine , supravalvular aortic stenosis , surgery , stenosis , aortic valve , cardiology , population , disease , environmental health
Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.