Open AccessA rare case of hypereosinophilic syndrome presenting with unilateral proptosis and torticollis
Author(s) -
Jayanta Kumar Das,
Krati Gupta,
Saurabh Deshmukh,
Richa Shrivastava
Publication year - 2018
Publication title -
indian journal of ophthalmology/indian journal of ophthalmology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 51
eISSN - 1998-3689
pISSN - 0301-4738
DOI - 10.4103/ijo.ijo_316_18
Subject(s) - medicine , hypereosinophilic syndrome , eosinophilia , torticollis , prednisolone , pathology , eosinophilic , dermatology , surgery
Hypereosinophilic syndrome (HES) is a spectrum of myeloproliferative disorder, which is characterized by persistent and marked blood eosinophilia and damage to multiple organs due to eosinophilic infiltration. Idiopathic HES is identified after ruling out all other causes of eosinophilia. Poor prognosis is usually associated with cardiac involvement and malignant transformation of blood cells. We report a rare case of HES in an 8-year-old boy who presented with unilateral proptosis and torticollis. The patient responded well to corticosteroid therapy with reduction of proptosis and torticollis and normalization of serum eosinophil count.