Open AccessIdiopathic pleuroparenchymal fibroelastosis: The first case to be managed with a successful lung transplant at King Faisal Specialist Hospital and Research Center, Riyadh
Author(s) -
Nour Abdullah Aljefri,
Fayha Farraj Abothenain,
Ahmed Hussein,
Waleed Saleh,
Khaled Alkattan,
Shamayel Mohammed,
Mohammed Alhajji
Publication year - 2019
Publication title -
annals of thoracic medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.639
H-Index - 33
eISSN - 1817-1737
pISSN - 1998-3557
DOI - 10.4103/atm.atm_106_18
Subject(s) - medicine , interstitial lung disease , lung , lung transplantation , idiopathic pulmonary fibrosis , surgery
Idiopathic Pleuro-Parenchymal Fibroelsatosis (PPFE) is a rare, progressive and recently recognized subtype of idiopathic interstitial lung disease with no recorded successful treatment other than lung transplant. We report a case of idiopathic pleuroparenchymal fibroelastosis from the Middle East, managed successfully by bilateral lung transplant performed on a 26 year old Saudi male.