Open AccessNeonatal supraventricular extrasystole as early clinical debut of cardiac rhabdomyoma
Author(s) -
Roger Esmel-Vilomara,
Amparo Castellote,
Luz Santana,
Dimpna C. Albert
Publication year - 2018
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/apc.apc_61_18
Subject(s) - rhabdomyoma , medicine , asymptomatic , magnetic resonance imaging , myxoma , cardiology , radiology , supraventricular arrhythmia , atrial fibrillation , tuberous sclerosis
We are reporting the case of a newborn with a diagnosis of frequent supraventricular extrasystoles, up to 25% of beats at Holter monitoring, and partial response to beta-blockers. Initial echocardiographic studies were normal until the identification of a right atrial mass at 4 months of life. Given the progressive growth of the mass and the suspicion of myxoma or thrombus in the magnetic resonance study, surgical resection of the tumor was performed. The surgical specimen was histologically diagnostic of rhabdomyoma. Currently, the patient remains asymptomatic after a 6-year follow-up period. A single rhabdomyoma is described, located in an atypical situation, near the crista terminalis, and diagnosed from frequent extrasystoles which appeared before the echocardiographic resolution was able to identify it. Magnetic resonance showed nondiagnostic tissue enhancement characteristics.