Open AccessIsolated agenesis of the right pulmonary veins with pulmonary sequestration
Author(s) -
Sandip Patil,
Sakshi Sachdeva,
Shweta Bakhru,
Bharat Dalvi,
Nageswara Rao Koneti
Publication year - 2019
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/apc.apc_55_18
Subject(s) - medicine , pulmonary sequestration , asymptomatic , right pulmonary artery , agenesis , shunt (medical) , cardiology , cardiac catheterization , pulmonary artery , lung , right to left shunt , right heart catheterization , radiology , surgery , percutaneous , patent foramen ovale
We report two cases of agenesis of the right pulmonary veins (PVs) associated with sequestration of the right lung with systemic to pulmonary collateral. Both the children were referred for evaluation of recurrent lower respiratory tract infections. Transthoracic echocardiographic evaluation showed reversal of flow in the right pulmonary artery (PA) and absent right PVs. Cardiac catheterization confirmed the diagnosis of agenesis of the right PVs. Transcatheter closure of collaterals was performed in view of significant shunt from systemic to PA. Both the patients are asymptomatic on follow-up.