Open AccessCaught-off guard: Unguarded mitral valve orifice in usual atrial arrangement with discordant atrioventricular connections and pulmonary atresia
Author(s) -
Nayan Banerji,
Mani Ram Krishna,
Raman Krishna Kumar,
Robert H. Anderson
Publication year - 2020
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/apc.apc_4_19
Subject(s) - medicine , cardiology , pulmonary atresia , body orifice , mitral valve , atrioventricular valve , atrioventricular septal defect , atresia , heart disease , anatomy , ventricle
Unguarding of an atrioventricular valvar orifice is a rare form of congenital heart disease that requires staged functionally univentricular palliation. Unguarding of the mitral valvar orifice has previously been reported in the setting of mirror-imaged atrial arrangement. We report a neonate with unguarding of the mitral valvar orifice in the setting of usual atrial arrangement, but with discordant atrioventricular connections and pulmonary atresia.