Open AccessPreliminary report of a true nasomaxillary infantile fibrosarcoma: Single-modality management and 2-year follow-up
Author(s) -
N. D. Jayakumar,
V. Rathnaprabhu,
S. Ramesh
Publication year - 2019
Publication title -
annals of maxillofacial surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.365
H-Index - 6
ISSN - 2231-0746
DOI - 10.4103/ams.ams_281_18
Subject(s) - medicine , histopathology , resection , surgical resection , fibrosarcoma , surgery , treatment modality , pathology
Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment involves surgical resection as primary modality. Prognosis is much better compared to the adult variant with even scope for spontaneous regression following "conservative" resection. We present a case of IFS of the nasomaxillary complex in a 3-month-old female child. We managed our case with surgical resection, and the patient has remained disease free for over 2 years.