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Sarcomatous transformation (Leiomyosarcoma) in polyostotic fibrous dysplagia
Author(s) -
MK Garg,
Rajinder Bhardwaj,
Srishti Gupta,
Navdeep Mann,
Simmi Kharb,
Aditi Pandit
Publication year - 2013
Publication title -
indian journal of endocrinology and metabolism
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.456
H-Index - 28
eISSN - 2230-9500
pISSN - 2230-8210
DOI - 10.4103/2230-8210.122645
Subject(s) - polyostotic fibrous dysplasia , medicine , chondrosarcoma , leiomyosarcoma , fibrous dysplasia , fibrosarcoma , sarcoma , malignant transformation , radiology , osteosarcoma , pathology
Malignant changes in polyostotic fibrous dysplasia are very rare. Most common malignancies reported are osteosarcoma and fibrosarcoma, chondrosarcoma and malignant fibrous histiocytoma. Here, we report a previously diagnosed case of fibrous dysplasia who has developed leiomyosarcoma; diagnosis of which was delayed for about one year despite repeated fine needle aspiration and open biopsy.

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