Open AccessPartial Anomalous Pulmonary Venous Return Presenting with Adult‐Onset Pulmonary Hypertension
Author(s) -
Sears Edmund H.,
Aliotta Jason M.,
Klinger James R.
Publication year - 2012
Publication title -
pulmonary circulation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.791
H-Index - 40
ISSN - 2045-8940
DOI - 10.4103/2045-8932.97637
Subject(s) - medicine , pulmonary hypertension , cardiology , rare disease , pulmonary veno occlusive disease , disease , pulmonary disease
Partial anomalous pulmonary venous return (PAPVR) is a rare cause of adult onset pulmonary arterial hypertension (PAH) that can present with a wide spectrum of severity from early childhood throughout adult life. We present two patients with PAH secondary to PAPVR who reflect this range of disease. The diagnosis and treatment of PAPVR and its role in pulmonary vascular disease is discussed. Cardiac and pulmonary physicians should be aware of this entity and its diagnosis and management options.