Open AccessNeglected primary Ewing′s sarcoma of ethmoid presenting as surgical emergency
Author(s) -
D. K. Shukla,
Vinjamuri Srinivas Rao,
Rajesh Alugolu,
A K Purohit
Publication year - 2013
Publication title -
asian journal of neurosurgery
Language(s) - English
Resource type - Journals
ISSN - 2248-9614
DOI - 10.4103/1793-5482.110281
Subject(s) - medicine , surgery , orbit (dynamics) , ewing's sarcoma , surgical decompression , decompression , visual acuity , ethmoid sinus , sarcoma , paranasal sinuses , pathology , chemotherapy , engineering , aerospace engineering
We present a male child with primary Ewing's sarcoma arising from ethmoid sinuses with intradural and extracranial extension (bilateral nasal cavities, orbits, and maxillary sinuses). This is a rare condition. He presented with recurrent episodes of epistaxis for 2 years, sudden onset rapidly progressive bilateral proptosis, with painful restriction of extraocular movements, and decreased visual acuity for 4 days. Sudden complete loss of vision following admission demanded emergency tumor decompression.