Open AccessRenal transplant in a tuberous sclerosis patient with bilateral giant renal angiomyolipomas and concurrent renal carcinoma
Author(s) -
Manzoor Hussain,
Muhammed Mubarak,
Gohar Sultan,
Ejaz Ahmed,
Mahira Yunus,
Mirza Ali Salehi,
Muhammad Asif,
Syeda Uzma Naqvi,
S. A. H. Rizvi
Publication year - 2013
Publication title -
saudi journal of kidney diseases and transplantation/našrat amraḍ wa zira'aẗ al-kulaẗ
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.268
H-Index - 30
eISSN - 2320-3838
pISSN - 1319-2442
DOI - 10.4103/1319-2442.109591
Subject(s) - tuberous sclerosis , medicine , angiomyolipoma , renal cell carcinoma , kidney , renal transplant , renal mass , renal function , pathology , urology , radiology , nephrectomy
Co-existence of angiomyolipoma (AML) and renal cell carcinoma (RCC) in the same tumor mass is very rare and only eight cases have been reported. We present a case of a young female with tuberous sclerosis complex (TSC) with bilateral huge renal AMLs. Both tumors were removed, one of which revealed co-incidental RCC. She was subsequently successfully transplanted a kidney from her brother and is maintaining normal graft function eight months post-transplant. No recurrence or metastases of RCC has been detected till the last follow-up.