Open AccessLipoid proteinosis: A review with two case reports
Author(s) -
Vishal Kabre,
Smitha Rani,
Keerthilatha M. Pai,
Sakshi Kamra
Publication year - 2015
Publication title -
contemporary clinical dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.289
H-Index - 21
eISSN - 0976-237X
pISSN - 0976-2361
DOI - 10.4103/0976-237x.156053
Subject(s) - hyaline , consanguinity , medicine , pathology , oral cavity , dermatology , pediatrics , dentistry
Lipoid proteinosis (LP) is a rare autosomal recessive genodermatoses characterized by deposition of amorphous hyaline material in different parts of the body, especially the skin, mucous membranes of the upper aerodigestive tract, and internal organs. Oral cavity is most extensively affected area by the disease. This paper reports two classic cases of LP with oral manifestations but without a history of consanguinity along with a concise review of the literature on the disease.