Open AccessPrune belly syndrome with urethral hypoplasia and vesico-cutaneous fistula: A case report and review of literature
Author(s) -
Osama Sarhan,
Mustafa S. Alghanbar,
Ziad Nakshabandi
Publication year - 2013
Publication title -
urology annals
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.355
H-Index - 20
eISSN - 0974-7834
pISSN - 0974-7796
DOI - 10.4103/0974-7796.120299
Subject(s) - medicine , hypoplasia , surgery , fistula , amniotic sac , fetus , pregnancy , amniotic fluid , biology , genetics
Association between Prune belly syndrome (PBS) and urethral hypoplasia is an unusual condition. It is usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with urethral hypoplasia and congenital vesico-cutaneous fistula in a male neonate. Patient underwent cutaneous vesicostomy and was discharged for close follow up of his renal function and for future reconstruction.