Open AccessProtein losing enteropathy secondary to a pulmonary artery stent
Author(s) -
Narayanswami Sreeram,
Uwe Trieschmann,
Gerardus Bennink
Publication year - 2012
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.93712
Subject(s) - medicine , cardiology , stent , protein losing enteropathy , enteropathy , pulmonary artery , cardiac catheterization , left pulmonary artery , hypoplastic left heart syndrome , stenosis , surgery , heart disease , disease
A 2-year-old patient with hypoplastic left heart syndrome presented 6 months following Fontan completion with protein-losing enteropathy (PLE). He had undergone stent implantation in the left pulmonary artery after the Norwood procedure, followed by redilation of the stent prior to Fontan completion. Combined bronchoscopic and catheterization studies during spontaneous breathing confirmed left bronchial stenosis behind the stent, and diastolic systemic ventricular pressure during expiration of 25 mm Hg. We postulate that the stent acts as a valve, against which the patient generates high expiratory pressures, which are reflected in the ventricular diastolic pressure. This may be the cause of PLE.