Open AccessModified pediatric Bentall procedure: A novel technique in a rare case
Author(s) -
Gananjay G. Salve,
Satish Javali,
Bharat Dalvi,
Krishnanaik Shivaprakash
Publication year - 2016
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.189124
Subject(s) - medicine , bentall procedure , ascending aorta , regurgitation (circulation) , asymptomatic , aortic root , surgery , aorta , cardiology
Aneurysms of ascending aorta are rarely seen in pediatric age group. Only few cases with Marfans syndrome have been reported in the literature. Preferred treatment for these children has been the standard Bentall procedure (aortic root replacement with composite graft prosthesis). We report a 4-year-old male child with huge aneurysm of ascending aorta and aortic root dilation with severe aortic regurgitation, having phenotypic features of Loeys-Dietz syndrome type I. He underwent Bentall procedure with a novel modification (medial trap-door technique for coronary reimplantation). Short-term result of this procedure is encouraging and he is asymptomatic for the last 14 months of follow-up.