Open AccessUhl′s anomaly: Absence of the right ventricular myocardium
Author(s) -
Joanna Ganczar,
Robert F. English
Publication year - 2015
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.149529
Subject(s) - medicine , cardiology , ventricle , ductus arteriosus , shunt (medical) , right atrium , ligation , pulmonary artery
We report a case of Uhl's anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was established with a myocardial biopsy.