Open AccessUncommon variants of the scimitar syndrome in two siblings
Author(s) -
I. Bo,
Piers E.F. Daubeney,
Michael L. Rigby
Publication year - 2015
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.149523
Subject(s) - scimitar syndrome , medicine , inferior vena cava , sibling , incidence (geometry) , cardiology , psychology , developmental psychology , physics , optics
The Scimitar syndrome is a complex association of cardiovascular and bronchopulmonary abnormalities, with the main feature a partial or total anomalous right pulmonary venous drainage to the inferior vena cava. A number of cases that lack of all the features of the typical syndrome have been described as Scimitar variant, but the incidence is rare. Familial occurrence is exceptional and limited to few cases in literature. We report two sibling diagnosed with an uncommon variant of the Scimitar syndrome.