Open AccessNon-cardiac issues in patients with heterotaxy syndrome
Author(s) -
Shyam Sunder Kothari
Publication year - 2014
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.140834
Subject(s) - medicine , heterotaxy , genitourinary system , intensive care medicine , asplenia , disease , polysplenia , heart disease , pediatrics , cardiology , spleen , situs inversus
Management of complex congenital heart disease in patients with Heterotaxy syndrome (HS) has steadily improved. However, there is an insufficient appreciation of various non-cardiac issues that might impact the overall status of these patients. This article briefly reviews the implications of gastrointestinal, immunologic, genitourinary, respiratory, and central nervous system involvement in HS patients with a view to aid in their comprehensive clinical management.