Open AccessYoung patient with generalized lymphangiomatosis: Differentiating the differential
Author(s) -
Tharani Putta,
Aparna Irodi,
Balamugesh Thangakunam,
Ashwin Oliver,
Rajesh Gunasingam
Publication year - 2016
Publication title -
indian journal of radiology and imaging - new series/indian journal of radiology and imaging/indian journal of radiology and imaging
Language(s) - English
Resource type - Journals
eISSN - 0971-3026
pISSN - 0970-2016
DOI - 10.4103/0971-3026.190416
Subject(s) - lymphangiomatosis , medicine , radiology , chest radiograph , mediastinum , differential diagnosis , thorax (insect anatomy) , mediastinal mass , presentation (obstetrics) , radiography , mediastinal lymphadenopathy , pleural effusion , lesion , computed tomography , thickening , lymphatic system , pathology , anatomy , chemistry , polymer science
We present the case of a 19-year-old man who was extensively evaluated in multiple centres for long-standing cough, dyspnea, and hemoptysis without a definitive diagnosis. His chest radiograph at presentation showed mediastinal widening, bilateral pleural effusions, and Kerley B lines. Computed tomography of the thorax showed a confluent, fluid-density mediastinal lesion enveloping the mediastinal viscera without any mass effect. There were bilateral pleural effusions, prominent peribronchovascular interstitial thickening, interlobular septal thickening and lobular areas of ground glass density with relative sparing of apices. There were a few dilated retroperitoneal lymphatics and well-defined lytic lesions in the bones. In this case report, we aim to systematically discuss the relevant differentials and arrive at a diagnosis. We also briefly discuss the treatment options and prognosis along with our patient's course in the hospital and final outcome.