Open AccessCombined mucopolysaccharidosis type VI and congenital adrenal hyperplasia in a child: Anesthetic considerations
Author(s) -
Abhishek Bansal,
Jayanta Das,
Raj Kumar,
Sangeeta Khanna,
Harsh Sapra,
Yatin Mehta
Publication year - 2012
Publication title -
journal of anaesthesiology-clinical pharmacology/journal of anaesthesiology clinical pharmacology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.466
H-Index - 32
eISSN - 2231-2730
pISSN - 0970-9185
DOI - 10.4103/0970-9185.98343
Subject(s) - medicine , anesthetic , pathophysiology , magnetic resonance imaging , hyperplasia , congenital adrenal hyperplasia , rare disease , mucopolysaccharidosis , disease , anesthesia , pediatrics , pathology , radiology
We present a child posted for magnetic resonance imaging of brain under general anesthesia with the rare combination of mucopolysachharidosis type VI and congenital adrenal hyperplasia. The presence of both these disorders has important anesthetic implications. The pathophysiology of this rare combination of disease is reviewed with emphasis on the anesthesia management.