Open AccessSuccessful anesthetic management of a child with blepharophimosis syndrome and atrial septal defect for reconstructive ocular surgery
Author(s) -
Dalim Kumar Baidya,
Puneet Khanna,
Anil Kumar,
Dilip Shende
Publication year - 2011
Publication title -
journal of anaesthesiology-clinical pharmacology/journal of anaesthesiology clinical pharmacology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.466
H-Index - 32
eISSN - 2231-2730
pISSN - 0970-9185
DOI - 10.4103/0970-9185.86607
Subject(s) - medicine , blepharophimosis , eyelid , airway management , surgery , airway , anesthesia , ptosis
Blepharophimosis syndrome is an autosomal dominant disorder characterized by eyelid malformation, involvement of reproductive system and abnormal facial morphology leading to difficult airway. We report a rare association of blepharophimosis syndrome and atrial septal defect in a 10-year-old girl who came for reconstruction surgery of eyelid. The child had dyspnea on exertion. Atrial septal defect was identified preoperatively by clinical examination and echocardiography. Anesthesia management was complicated by failure in laryngeal mask airway placement and Cobra perilaryngeal airway was subsequently used.