Open AccessPriapism associated with Niemann-Pick disease in a 15-year-old boy
Author(s) -
Manjunath Shetty,
M. Sunil Kumar,
T. K. Sen
Publication year - 2011
Publication title -
indian journal of urology/indian journal of urology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.333
H-Index - 30
eISSN - 1998-3824
pISSN - 0970-1591
DOI - 10.4103/0970-1591.85452
Subject(s) - priapism , medicine , niemann–pick disease , disease , surgery , bone marrow , pediatrics
A 15-year-old boy presented with priapism of 46 h duration. There was no known cause of priapism detected in him. During evaluation, biopsy of the lymph node and bone marrow aspiration detected patient to be having Niemann-Pick disease. He was managed with cavernous aspiration, saline irrigation, and intracavernosal phenylephrine injection. Although priapism is associated with many known diseases, about half of the cases are of idiopathic origin. We are reporting the first case of priapism associated with Niemann-Pick disease in the literature.