Open AccessPrimary intratesticular rhabdomyosarcoma in pediatrics
Author(s) -
Jitendra G Nasit,
Biren Parikh,
Priti Trivedi,
Minit Shah
Publication year - 2013
Publication title -
indian journal of urology/indian journal of urology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.333
H-Index - 30
eISSN - 1998-3824
pISSN - 0970-1591
DOI - 10.4103/0970-1591.109995
Subject(s) - medicine , rhabdomyosarcoma , embryonal rhabdomyosarcoma , germ cell , radiation therapy , metastasis , germ cell tumors , oncology , sarcoma , pathology , chemotherapy , cancer research , cancer , biochemistry , chemistry , gene
Testicular sarcomas constitute only 1-2% of all testicular tumors and are mostly associated with germ cell tumor. Primary intratesticular rhabdomyosarcoma is rare and only 14 cases have been reported in the literature till date. It should be differentiated from germ cell tumor with sarcomatous component, other intratesticular spindle-cell sarcomas and paratesticular rhabdomyosarcoma. Accurate diagnosis and early treatment is essential as it is an aggressive tumor with high metastatic potential and poor prognosis. Orchidectomy is the treatment of choice. Chemo-radiotherapy is recommended in case of recurrence and metastasis.