Open AccessEctodermal dysplasia - Maxillary and mandibular alveolar reconstruction with dental rehabilitation: A case report and review of the literature
Author(s) -
Sanjeev N. Deshpande,
Vikas Kumar
Publication year - 2010
Publication title -
indian journal of plastic surgery/indian journal of plastic surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.299
H-Index - 29
eISSN - 1998-376X
pISSN - 0970-0358
DOI - 10.4103/0970-0358.63969
Subject(s) - ectodermal dysplasia , medicine , hypodontia , hypohidrotic ectodermal dysplasia , anodontia , dentistry , osseointegration , rehabilitation , orthodontics , mandible (arthropod mouthpart) , aplasia , dermatology , surgery , implant , physical therapy , botany , biology , genus
Ectodermal dysplasia is a rare group of inherited disorders characterized by aplasia or dysplasia of tissues of ectodermal origin, such as hair, nails, teeth and skin. Dental manifestations include hypodontia, complete anodontia or malformed teeth. Oral rehabilitation is the major surgical challenge in such patients. It frequently requires alveolar reconstruction followed by dental implants. We report a case of hypohidrotic ectodermal dysplasia, which was managed with reconstruction of both the upper and the lower alveolus using free fibula flaps with dental rehabilitation using osseointegrated implants.