Open AccessDyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
Author(s) -
Anshuman Singh,
VK Pandey,
Manish Tandon,
Chandra Kant Pandey
Publication year - 2015
Publication title -
indian journal of anaesthesia/indian journal of anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.645
H-Index - 30
eISSN - 0976-2817
pISSN - 0019-5049
DOI - 10.4103/0019-5049.156888
Subject(s) - medicine , dyskeratosis congenita , liver transplantation , cirrhosis , hepatopulmonary syndrome , perioperative , transplantation , liver disease , surgery , gastroenterology , dna , genetics , telomere , biology
Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation.