Open AccessSpontaneous hemothorax: A rare lethal pulmonary complication of neurofibromatosis type 1
Author(s) -
Aditya Nath Shukla,
Ashok Kumar Singh,
Saket Nigam
Publication year - 2021
Publication title -
indian journal of case reports
Language(s) - English
Resource type - Journals
eISSN - 2454-1303
pISSN - 2454-129X
DOI - 10.32677/ijcr.v7i10.3062
Subject(s) - medicine , neurofibromatosis , hemothorax , complication , neurofibromatosis type i , disease , surgery , shock (circulatory) , pathology , radiology , pneumothorax
Neurofibromatosis 1 (NF1), also called von Recklinghausen’s disease, is an autosomal dominant disease characterized by multiple non-cancerous tumors of nerves and skin, and areas of abnormal pigmentation. Vasculopathy and spontaneous hemothorax are rare complications, but potentially lethal, which necessitates quick and decisive intervention to save the life of the patient. Here, we present a case of spontaneous massive haemothorax leading to hemorrhagic shock in a 66-year-old woman with neurofibromatosis type-1. She was investigated and managed successfully.