Open AccessA Retrospective Case Study of 13 Uterine Perivascular Epithelioid Cell Neoplasm (PEComa) Patients
Author(s) -
Jiahui Gu,
Wantong Wang,
Shizhuo Wang
Publication year - 2021
Publication title -
oncotargets and therapy
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.054
H-Index - 60
ISSN - 1178-6930
DOI - 10.2147/ott.s300523
Subject(s) - medicine , perivascular epithelioid cell , pathological , adjuvant therapy , uterus , immunohistochemistry , chemotherapy , medical record , leiomyosarcoma , leiomyoma , epithelioid cell , surgery , radiology , pathology
Perivascular epithelioid cell neoplasms (PEComas) are rare mesenchymal tumors that originate from perivascular epithelioid cells. The uterus is the second most common organ to be affected by PEComa. Most PEComas are benign and the prognosis is usually good. Surgery is the main treatment at present, and adjuvant therapy is mainly used for malignant cases. However, because of the lack of described cases, the best diagnosis and treatment of these tumors cannot be determined.