Open AccessAcute Plasma Cell Leukemia Presenting as Primary Hyperammonemic Encephalopathy
Author(s) -
Dveet Patel,
Andrew Mangano,
David Moccia,
Shawn Esperti,
Kunjan Udani,
Jordan Henderson,
Nino Balanchivadze
Publication year - 2020
Publication title -
journal of medical cases
Language(s) - Uncategorized
Resource type - Journals
eISSN - 1923-4163
pISSN - 1923-4155
DOI - 10.14740/jmc3559
Subject(s) - medicine , plasma cell leukemia , presentation (obstetrics) , encephalopathy , multiple myeloma , rare disease , pediatrics , gastroenterology , disease , surgery
Primary plasma cell leukemia (PPCL) is a rare form of multiple myeloma (MM) and is a rare aggressive disease with a median overall survival of 6 - 11 months. We present a case of acute hyperammonemic encephalopathy as the initial presentation of PPCL in a 78-year-old woman to highlight an atypical presentation of this disorder.