Open AccessIntracardiac Extension of Wilms Tumor: A Case of a 2.5-Year-Old Girl Presenting with Upper Venous Congestion Caused by Tumor Growth into the Right Cardiac Ventricle
Author(s) -
Roland Imle,
Georgi Tosev,
Wolfgang Behnisch,
JensPeter Schenk,
Helmut Rauch,
Andreas S. Mueller,
Matthias Gorenflo,
Tsvetomir Loukanov,
Andreas E. Kulozik,
Joanne NyarangiDix
Publication year - 2019
Publication title -
case reports in oncology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.365
H-Index - 19
ISSN - 1662-6575
DOI - 10.1159/000496020
Subject(s) - medicine , intracardiac injection , ventricle , vincristine , median sternotomy , wilms' tumor , laparotomy , surgery , cardiopulmonary bypass , thoracotomy , circulatory system , chemotherapy , cardiology , radiology , cyclophosphamide
While Wilms tumors (WT) typically present solely with an abdominally palpable mass, rare cases exhibiting vascular tumor growth can also present with circulatory problems. Here, we report the case of a 2.5-year-old girl presenting with upper venous congestion and arterial hypertension as the primary symptoms of intraventricular tumor growth exhibiting remarkable tubular and perfused morphology. Clinical situation stabilized after initiation of neoadjuvant chemotherapy (NAC) with actinomycin D and vincristine, followed by surgical resection via laparotomy and sternotomy supported by cardiopulmonary bypass and deep hypothermia. Our results highlight the previously reported feasibility of this approach, even in primarily unstable patients.