Open AccessPeroral Endoscopic Myotomy in Diffuse Thickened Esophageal Wall in an Adolescent
Author(s) -
А. А. Смирнов,
А. Н. Бураков,
А. Н. Швецов,
Е. В. Блинов,
К. Д. Семенихин,
Н. В. Конкина,
Sergey Y Dvoreckij
Publication year - 2018
Publication title -
case reports in gastroenterology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.247
H-Index - 18
ISSN - 1662-0631
DOI - 10.1159/000492212
Subject(s) - achalasia , medicine , myotomy , esophageal spasm , gold standard (test) , esophagus , heller myotomy , leiomyoma , thickening , radiology , surgery , chemistry , polymer science
Achalasia is an extremely rare pathology in children. Peroral endoscopic myotomy (POEM) is the gold standard for the surgical treatment of achalasia in adults, but only a limited number of cases of achalasia treatment using POEM in children have been published in the literature. Sometimes, high-resolution manometry signs of achalasia can mimic diffuse esophageal leiomyoma. This case report represents the first known successful performance of POEM on a 15-year-old female with diffuse thickening of the esophagus with signs and symptoms of achalasia and suspicion for Alport syndrome associated with diffuse esophageal leiomyoma.