Surviving male with incontinentia pigmenti: a case report

Summary.  Incontinentia pigmenti, or Block–Sulzberger Syndrome, is an X‐linked dominant disorder with characteristic skin, hair, eye and tooth abnormalities. It is classically considered a male‐lethal disorder with recurrent miscarriages of male foetuses. A few cases of surviving males with incontinentia pigmenti have been reported in the medical literature. This article reports the medical and dental findings of a boy diagnosed with incontinentia pigmenti.