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Distinct proteostasis states drive pharmacologic chaperone susceptibility for cystic fibrosis transmembrane conductance regulator misfolding mutants
Author(s) -
Eli Fritz McDonald,
Carleen Mae P. Sabusap,
MinSoo Kim,
Lars Plate
Publication year - 2022
Publication title -
molecular biology of the cell
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 2.463
H-Index - 225
eISSN - 1939-4586
pISSN - 1059-1524
DOI - 10.1091/mbc.e21-11-0578
Subject(s) - proteostasis , cystic fibrosis transmembrane conductance regulator , biology , regulator , cystic fibrosis , mutant , microbiology and biotechnology , chaperone (clinical) , negative regulator , transmembrane protein , protein folding , genetics , signal transduction , pathology , gene , medicine , receptor

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