Open AccessAtriofascicular Mahaim with Ebstein anomaly: A case report
Author(s) -
Ueshima Kazushi,
Nakamura Yoshihide,
Takeno Satoru,
Miyake Toshiharu,
Takemura Tsukasa
Publication year - 2017
Publication title -
journal of arrhythmia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.463
H-Index - 21
eISSN - 1883-2148
pISSN - 1880-4276
DOI - 10.1016/j.joa.2017.06.007
Subject(s) - medicine , cardiology , qrs complex , left bundle branch block , accessory pathway , tachycardia , atrial fibrillation , heart failure , catheter ablation
We report a case of a 7‐year‐old girl with atriofascicular Mahaim (AFM) pathway concomitant with Ebstein's anomaly. The QRS wave showed left bundle branch block pattern on electrocardiogram. Holter electrocardiogram showed prolongation of the PR interval and QRS morphological change during sinus tachycardia. An electrophysiological study demonstrated that the distal His potential appeared earlier than the proximal His potential, which suggested retrograde His conduction toward the atrioventricular node. Conduction from the Mahaim fiber to the His bundle was faster than that from the atrioventricular node towards the His bundle. The findings of this important case allowed a differential diagnosis between AFM and Wolff‐Parkinson‐White (WPW) syndrome.