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Clinical response to sildenafil in pulmonary hypertension associated with Gaucher disease
Author(s) -
Fernandes C. J. C.,
Jardim C.,
Carvalho L. A. S.,
Farias A. Q.,
Filho M. Terra,
Souza R.
Publication year - 2005
Publication title -
journal of inherited metabolic disease
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.462
H-Index - 102
eISSN - 1573-2665
pISSN - 0141-8955
DOI - 10.1007/s10545-005-0603-y
Subject(s) - sildenafil , medicine , pulmonary hypertension , disease , gaucher's disease , human genetics , cardiology , gene , biochemistry , chemistry
Summary There are few reports of pulmonary hypertension in Gaucher disease. We report a patient who showed significant clinical improvement after treatment with sildenafil.