
S wyer‐ J ames syndrome associated with asthma and a giant bulla
Author(s) -
Kayawake Hidenao,
Sakai Hiroaki,
Matsumoto Hisako,
Date Hiroshi
Publication year - 2014
Publication title -
respirology case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.304
H-Index - 9
ISSN - 2051-3380
DOI - 10.1002/rcr2.82
Subject(s) - medicine , pneumothorax , bulla (seal) , asthma , exertional dyspnea , surgery , lung
S wyer‐ J ames syndrome was first described in 1953 as unilateral pulmonary emphysema in a 6‐year‐old boy. The characteristic feature of this syndrome is unilateral pulmonary hyperlucency on a chest X ‐ray film. Typical symptoms include recurrent chest infections, chronic cough, wheezing, and exertional dyspnea. Although there have been a few reports of pneumothorax in patients with S wyer‐ J ames syndrome, there have been no reports about an association with giant bullae. Here, we report a case of S wyer‐ J ames syndrome associated with a giant bulla and asthma, in which surgery achieved marked improvement of dyspnea.