Open AccessA rare case of severe right heart failure due to pulmonary artery lymphomatoid granulomatosis
Author(s) -
Su Hongling,
Wei Rong,
Duan Yichao,
Guo Zhaoxia,
Wang Aqian,
Jiang Na,
Li Wanpeng,
Zhu Yan,
Guo Yanqing,
Zhang Min,
Zhang Yan,
Cao Yunshan
Publication year - 2020
Publication title -
esc heart failure
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.787
H-Index - 25
ISSN - 2055-5822
DOI - 10.1002/ehf2.13000
Subject(s) - medicine , lymphomatoid granulomatosis , percutaneous , pulmonary artery , heart failure , right heart failure , cardiology , rare disease , pulmonary veno occlusive disease , stenosis , radiology , surgery , lung , disease , pulmonary hypertension
Lymphomatoid granulomatosis is a rare, vascular‐centric, and vessel‐destroying lymphoproliferative disease that hardly involves the pulmonary arteries. Herein, we report a case with severe right heart failure and pulmonary arterial stenosis caused by pulmonary artery lymphomatoid granulomatosis. This case was diagnosed by percutaneous transluminal pulmonary artery biopsy and was effectively treated with stent implantation and steroid administration.