Open AccessSuccessful outcome of three patients with sickle‐cell disease and fat embolism syndrome treated with intensive exchange transfusion
Author(s) -
Greaves Paul,
Mathew Vivek,
Peters Catherine,
Rowe Susan,
Amos Roger J.,
Tsitsikas Dimitris A.
Publication year - 2017
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.727
Subject(s) - medicine , exchange transfusion , disease , intensive care medicine , fat embolism syndrome , fat embolism , pediatrics
Key Clinical Message Fat embolism syndrome ( FES ) is a rare complication of sickle‐cell disease ( SCD ) associated with extremely high mortality rates. It affects predominantly non‐ SS patients and those with previously mild disease. Rapid institution of exchange transfusion with an aim to reduce HbS to very low levels as soon as FES is suspected can be life‐saving.